Benign vulvar vestibular papillomatosis: An underreported condition in Indian dermatological literature

Indian Dermatology Online Journal | January-February 2017 | Vol 8 | Issue 1 63 Other differential diagnosis to be considered for such distinctive skin lesions are connective tissue nevi, localized amyloidosis, and papular mucinosis. Connective tissue nevus can occur at different sites as compared to the patterned distribution of skin lesions in Hunter’s syndrome. Lack of inflammation and pruritus would rule against amyloidosis. Mucinosis presents as translucent firm papules and nodules.[1] “Pebbled skin” is a pathognomic sign of Hunter syndrome and is not seen in other types of MPS. Recognition of this entity can provide a clue to diagnose milder forms of the disease as it can be the earliest clinical feature, which helps in counseling the family.